Adamantinomatous craniopharyngioma of cerebellopontine angle in association with Gardner’s syndrome

Background. Craniopharyngiomas are benign epithelial tumors. According to embryogenetic theory, these neoplasms develop from the remains of cells Rathke’s pouch, which connects cavities primary oral tube with pituitary gland in embryonic period. The metaplastic theory assumes occurrence craniopharyngiomas as a result metaplasia chiasmal-sellar region. Objective. To present clinical case ectopic adamantium-like craniopharyngioma right cerebellopontine angle associated Gardner’s syndrome. Design and methods. analysis SCT, MRI, histological, histochemical other special studies, well data four similar observations published literature, was carried out. Results. We describe rare syndrome (familial adenomatous polyposis, multiple skull osteomas soft tissue tumors) diagnosed 27-year-old patient. It is noted, while inexplicable, correlation patients region angle. Conclusions. In adamantine-like craniopharyngiomas, including collection family history studies exclude intestinal polyposis Gardner complex treatment diagnostics id highly recommended.